| CODE LIST | 
- 
- CODES:
 
- 
- 
- CODE DESCRIPTION:    
Severe combined immunodeficiency due to absent peripheral T cell maturation 
(disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Severe combined immunodeficiency due to absent lymphoid stem cells (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Acquired neutropenia in newborn (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Cyclical neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
X-linked severe combined immunodeficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
X-linked hypogammaglobulinemia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chronic benign neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Metabolic neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Autoimmune neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Corticosteroid-induced neutrophilia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Myeloperoxidase deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Hemolytic erythrophagocytic syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Common variable agammaglobulinemia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Hemophagocytic lymphohistiocytosis (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunodeficiency disorder (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
X-linked agammaglobulinemia with growth hormone deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Autosomal agammaglobulinemia with absent B-cells (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunoglobulin heavy chain deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Selective immunoglobulin E deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Selective immunoglobulin D deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Selective immunoglobulin M and immunoglobulin A deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunoglobulin light chain deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunoglobulin subclass deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Aplasia of thymus gland with immunodeficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunoglobulin G2 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Combined immunoglobulin G2 and G4 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunoglobulin G3 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunoglobulin G4 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunoglobulin G1 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunoglobulin A1 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunoglobulin A2 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunoglobulin-associated molecule deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Secretory piece deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Defective immunoglobulin glycosylation (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Disorder of complement (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Specific antibody deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Anti-polysaccharide antibody deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Anti-haemophilus influenzae B polysaccharide antibody deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Anti-pneumococcal polysaccharide antibody deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Anti-meningococcal polysaccharide A antibody deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Anti-meningococcal polysaccharide C antibody deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Anti-protein antibody deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Anti-staphylococcal antibody deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Primary immunoglobulin catabolism abnormality (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunoglobulin hypercatabolism (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement deficiency disease (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Familial immunoglobulin hypercatabolism (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Severe combined immunodeficiency with maternofetal engraftment (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Warts, hypogammaglobulinemia, infections, and myelokathexis (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Benign combined immunodeficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Phagocytic cell defect (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Disorder of phagocytic cell number (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chronic familial neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Lipochrome histiocytosis - familial (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Defective phagocytic cell opsonization (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Mannan-binding protein deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Myelokathexis (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Defective phagocytic cell chemotaxis (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Defective phagocytic cell adhesion (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Leukocyte adhesion deficiency - type 1 (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Leukocyte adhesion deficiency - type 2 (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Tuftsin deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Defective phagocytic cell killing (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Leukocyte glucose-6-phosphate dehydrogenase deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Neutrophil lactoferrin deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Neutrophil secondary granule deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Glutathione synthetase deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Lymphopenic agammaglobulinemia - short-limbed dwarfism syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Gluthathione peroxidase deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Combined phagocytic defect (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Classical complement pathway abnormality (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 1q deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 1q beta chain deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 1q dysfunction (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 1r deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 1s deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 2 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 4 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chronic granulomatous disease, type IIA (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 4A deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 4B deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 3 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Alternative pathway deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Factor B deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Factor D deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Terminal component deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 5 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 6 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 7 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunoglobulin A deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Combined complement 6 and 7 deficiencies (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 8 beta chain deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 8 beta chain dysfunction (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 8 alpha-gamma deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 9 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement regulatory factor defect (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Hereditary C1 esterase inhibitor deficiency - deficient factor (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Hereditary C1 esterase inhibitor deficiency - dysfunctional factor (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Factor I deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Factor H deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chronic granulomatous disease, type I (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 4 binding protein deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Decay accelerating factor deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Homologous restriction factor deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 5a inhibitor deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Anaphylotoxin inactivator deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement receptor deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement receptor 1 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement receptor 3 deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunodeficiency with major anomalies (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunodeficiency associated with chromosomal abnormality (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Non dose-related drug-induced neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Severe combined immunodeficiency disease (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Centromeric instability of chromosomes 1,9 and 16 and immunodeficiency 
(disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chromosome 18 syndromes and antibody deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chromosome 22 abnormalities with hypogammaglobulinemia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Monosomy 22 and absence of immunoglobulin A (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Deletion of X-chromosome and hypogammaglobulinemia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Microcephaly, normal intelligence and immunodeficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Triple X syndrome, epilepsy, and hypogammaglobulinemia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
18-p syndrome with associated immunodeficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunodeficiency associated with multiple organ system abnormalities (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Age-related immunodeficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Toxic neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Transient immunodeficiency of infancy (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Drug-induced immunodeficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Acquired C1 esterase inhibitor deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Familial neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chronic idiopathic neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement 5 dysfunction (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Agranulocytopenic disorder (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Neutropenia due to irradiation (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Functional disorders of polymorphonuclear neutrophils (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chloramphenicol-induced neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Secondary immune deficiency disorder (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Phagocytic cell dysfunction (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Neutropenic disorder (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
De Vaal's syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Reticular dysgenesis with congenital aleukocytosis (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Acquired immunodeficiency syndrome with dermatomycosis (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Autosomal recessive severe combined immunodeficiency disease (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement component deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Congenital immunodeficiency involving the hematopoietic system (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chronic granulomatous disease (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Familial hemophagocytic lymphohistiocytosis (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Wiskott-Aldrich syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunodeficiency with multicarboxylase deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
B-lymphocyte immunodeficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
T-lymphocyte immunodeficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Wiskott-Aldrich autosomal dominant variant syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Febrile neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Neutrophilia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Neutropenia associated with acquired immunodeficiency syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunoglobulin deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Agranulocytosis associated with acquired immunodeficiency syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chemotherapy-induced neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Congenital immunodeficiency disease (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Combined immunodeficiency disease (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Severe combined immunodeficiency due to absent adenosine deaminase (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Hypopigmentation-immunodeficiency disease (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Familial C3B inhibitor deficiency syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chronic granulomatous disease, type IA (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Neutropenia with dysgranulopoiesis (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Bloom syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Adenosine deaminase deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Severe combined immunodeficiency due to absent interleukin-2 production 
(disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Kappa light chain disease (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Neutropenia associated with infectious disease (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Acute neutrophilia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Drug-induced neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Dysplasia of thymus gland with immunodeficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Severe combined immunodeficiency due to absent T cell receptor (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Job's syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Transient neonatal neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunoglobulinemia with isolated somatotropin deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Nezelof's syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Dose-related drug-induced neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Congenital hypergammaglobulinemia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Primary immune deficiency disorder (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Purine-nucleoside phosphorylase deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Acquired immune deficiency syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Drug-induced neutrophilia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immune neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
X-linked agammaglobulinemia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Lambda light chain disease (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunodeficiency with thymoma (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Ataxia-telangiectasia syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Pseudoneutrophilia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Lazy leukocyte syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Neutrophilic leukemoid reaction (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Severe combined immunodeficiency due to absent class II human leukocyte 
antigens (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Agranulocytic angina (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chronic granulomatous disease, type IVA (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Acquired immunodeficiency syndrome with Salmonella infection (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
X-linked lymphoproliferative syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chronic granulomatous disease, type II (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Alloimmune neonatal neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Congenital leukocyte adherence deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Isoimmune neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chronic neutrophilia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Properdin deficiency disease (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Hyperimmunoglobulin M syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chronic granulomatous disease, type III (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Hereditary angioedema (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Transient hypogammaglobulinemia of infancy (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Shwachman syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Congenital neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Agranulocytosis (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunodeficiency secondary to neoplasm (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunodeficiency secondary to trauma (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunodeficiency secondary to corticosteroids (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunodeficiency secondary to radiation therapy (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunodeficiency secondary to chemotherapy (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Quantitative disorder of neutrophils (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Quantitative abnormality of granulocytes (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chdiak-Higashi syndrome (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Reticular dysgenesis (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Neutropenia associated with autoimmune disease (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Complement abnormality (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Severe combined immunodeficiency due to absent interleukin-2 receptor (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Congenital agammaglobulinemia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Stress neutrophilia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Hereditary neutrophilia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chronic benign neutropenia of childhood (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chronic idiopathic immunoneutropenia in adults (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chronic hypoplastic neutropenia (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Selective immunoglobulin A deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Selective immunoglobulin M deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Selective immunoglobulin G deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Chronic granulomatous disease, type IV (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Autosomal recessive severe combined immunodeficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Thymic aplasia or dysplasia with immunodeficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Severe combined immunodeficiency with reticular dysgenesis (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Severe combined immunodeficiency with low T- and B-cell numbers (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Severe combined immunodeficiency with low or normal B-cell numbers (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Major histocompatibility complex class I deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Major histocompatibility complex class II deficiency (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Immunodeficiency following hereditary defective response to Epstein-Barr 
virus (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Lymphocyte function antigen-1 defect (disorder)
 
 
 
- 
- CODE DESCRIPTION:    
Primary splenic neutropenia (disorder)
 
 
 
 
  
 
- 
- CODES:
 
- 
- 
- CODE DESCRIPTION:    
Selective IgA immunodeficiency
 
 
 
- 
- CODE DESCRIPTION:    
Nezelof's syndrome
 
 
 
- 
- CODE DESCRIPTION:    
Other deficiency of cell-mediated immunity
 
 
 
- 
- CODE DESCRIPTION:    
Combined immunity deficiency
 
 
 
- 
- CODE DESCRIPTION:    
Unspecified immunity deficiency
 
 
 
- 
- CODE DESCRIPTION:    
Autoimmune lymphoproliferative syndrome
 
 
 
- 
- CODE DESCRIPTION:    
Autoimmune disease, not elsewhere classified
 
 
 
- 
- CODE DESCRIPTION:    
Acute graft-versus-host disease
 
 
 
- 
- CODE DESCRIPTION:    
Chronic graft-versus-host disease
 
 
 
- 
- CODE DESCRIPTION:    
Acute on chronic graft-versus-host disease
 
 
 
- 
- CODE DESCRIPTION:    
Other specified disorders involving the immune mechanism
 
 
 
- 
- CODE DESCRIPTION:    
Selective IgM immunodeficiency
 
 
 
- 
- CODE DESCRIPTION:    
Unspecified disorder of immune mechanism
 
 
 
- 
- CODE:    279.00
 
- CODE DESCRIPTION:    
Hypogammaglobulinemia, unspecified
 
 
 
- 
- CODE:    279.10
 
- CODE DESCRIPTION:    
Immunodeficiency with predominant T-cell defect, unspecified
 
 
 
- 
- CODE:    279.50
 
- CODE DESCRIPTION:    
Graft-versus-host disease, unspecified
 
 
 
- 
- CODE DESCRIPTION:    
Other selective immunoglobulin deficiencies
 
 
 
- 
- CODE DESCRIPTION:    
Congenital hypogammaglobulinemia
 
 
 
- 
- CODE DESCRIPTION:    
Immunodeficiency with increased IgM
 
 
 
- 
- CODE DESCRIPTION:    
Common variable immunodeficiency
 
 
 
- 
- CODE DESCRIPTION:    
Other deficiency of humoral immunity
 
 
 
- 
- CODE DESCRIPTION:    
Digeorge's syndrome
 
 
 
- 
- CODE DESCRIPTION:    
Wiskott-aldrich syndrome
 
 
 
 
  
 
- 
- CODES:
 
- 
- 
- CODE:    D80.0
 
- CODE DESCRIPTION:    
Hereditary hypogammaglobulinemia
 
 
 
- 
- CODE:    D80.9
 
- CODE DESCRIPTION:    
Immunodeficiency with predominantly antibody defects, unspecified
 
 
 
- 
- CODE:    D81.0
 
- CODE DESCRIPTION:    
Severe combined immunodeficiency [SCID] with reticular dysgenesis
 
 
 
- 
- CODE:    D81.1
 
- CODE DESCRIPTION:    
Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
 
 
 
- 
- CODE:    D81.2
 
- CODE DESCRIPTION:    
Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
 
 
 
- 
- CODE:    D81.4
 
- CODE DESCRIPTION:    
Nezelof's syndrome
 
 
 
- 
- CODE:    D81.6
 
- CODE DESCRIPTION:    
Major histocompatibility complex class I deficiency
 
 
 
- 
- CODE:    D81.7
 
- CODE DESCRIPTION:    
Major histocompatibility complex class II deficiency
 
 
 
- 
- CODE:    D81.89
 
- CODE DESCRIPTION:    
Other combined immunodeficiencies
 
 
 
- 
- CODE:    D81.9
 
- CODE DESCRIPTION:    
Combined immunodeficiency, unspecified
 
 
 
- 
- CODE:    D82.0
 
- CODE DESCRIPTION:    
Wiskott-Aldrich syndrome
 
 
 
- 
- CODE:    D80.1
 
- CODE DESCRIPTION:    
Nonfamilial hypogammaglobulinemia
 
 
 
- 
- CODE:    D82.1
 
- CODE DESCRIPTION:    
Di George's syndrome
 
 
 
- 
- CODE:    D82.2
 
- CODE DESCRIPTION:    
Immunodeficiency with short-limbed stature
 
 
 
- 
- CODE:    D82.3
 
- CODE DESCRIPTION:    
Immunodeficiency following hereditary defective response to Epstein-Barr virus
 
 
 
- 
- CODE:    D82.4
 
- CODE DESCRIPTION:    
Hyperimmunoglobulin E [IgE] syndrome
 
 
 
- 
- CODE:    D82.8
 
- CODE DESCRIPTION:    
Immunodeficiency associated with other specified major defects
 
 
 
- 
- CODE:    D82.9
 
- CODE DESCRIPTION:    
Immunodeficiency associated with major defect, unspecified
 
 
 
- 
- CODE:    D83.0
 
- CODE DESCRIPTION:    
Common variable immunodeficiency with predominant abnormalities of B-cell 
numbers and function
 
 
 
- 
- CODE:    D83.1
 
- CODE DESCRIPTION:    
Common variable immunodeficiency with predominant immunoregulatory T-cell 
disorders
 
 
 
- 
- CODE:    D83.2
 
- CODE DESCRIPTION:    
Common variable immunodeficiency with autoantibodies to B- or T-cells
 
 
 
- 
- CODE:    D83.8
 
- CODE DESCRIPTION:    
Other common variable immunodeficiencies
 
 
 
- 
- CODE:    D80.2
 
- CODE DESCRIPTION:    
Selective deficiency of immunoglobulin A [IgA]
 
 
 
- 
- CODE:    D83.9
 
- CODE DESCRIPTION:    
Common variable immunodeficiency, unspecified
 
 
 
- 
- CODE:    D84.0
 
- CODE DESCRIPTION:    
Lymphocyte function antigen-1 [LFA-1] defect
 
 
 
- 
- CODE:    D84.1
 
- CODE DESCRIPTION:    
Defects in the complement system
 
 
 
- 
- CODE:    D84.8
 
- CODE DESCRIPTION:    
Other specified immunodeficiencies
 
 
 
- 
- CODE:    D84.9
 
- CODE DESCRIPTION:    
Immunodeficiency, unspecified
 
 
 
- 
- CODE:    D89.3
 
- CODE DESCRIPTION:    
Immune reconstitution syndrome
 
 
 
- 
- CODE:    D89.810
 
- CODE DESCRIPTION:    
Acute graft-versus-host disease
 
 
 
- 
- CODE:    D89.811
 
- CODE DESCRIPTION:    
Chronic graft-versus-host disease
 
 
 
- 
- CODE:    D89.812
 
- CODE DESCRIPTION:    
Acute on chronic graft-versus-host disease
 
 
 
- 
- CODE:    D89.813
 
- CODE DESCRIPTION:    
Graft-versus-host disease, unspecified
 
 
 
- 
- CODE:    D80.3
 
- CODE DESCRIPTION:    
Selective deficiency of immunoglobulin G [IgG] subclasses
 
 
 
- 
- CODE:    D89.82
 
- CODE DESCRIPTION:    
Autoimmune lymphoproliferative syndrome [ALPS]
 
 
 
- 
- CODE:    D89.89
 
- CODE DESCRIPTION:    
Other specified disorders involving the immune mechanism, not elsewhere 
classified
 
 
 
- 
- CODE:    D89.9
 
- CODE DESCRIPTION:    
Disorder involving the immune mechanism, unspecified
 
 
 
- 
- CODE:    D80.4
 
- CODE DESCRIPTION:    
Selective deficiency of immunoglobulin M [IgM]
 
 
 
- 
- CODE:    D80.5
 
- CODE DESCRIPTION:    
Immunodeficiency with increased immunoglobulin M [IgM]
 
 
 
- 
- CODE:    D80.6
 
- CODE DESCRIPTION:    
Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia
 
 
 
- 
- CODE:    D80.7
 
- CODE DESCRIPTION:    
Transient hypogammaglobulinemia of infancy
 
 
 
- 
- CODE:    D80.8
 
- CODE DESCRIPTION:    
Other immunodeficiencies with predominantly antibody defects
 
 
 
 
  
 
 
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